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Cystic fibrosis, PKU and the Digestive system

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Cystic fibrosis, PKU and the Digestive system
Cystic fibrosis, PKU and the Digestive system

1. What are the symptoms of cystic fibrosis and PKU with respect to the digestive system?

Symptoms for cystic fibrosis include diarrhea that does not go away, foul-smelling stools, greasy stools, frequent urinating, frequent episodes of Pneumonia, persistent cough, skin tastes like salt, poor growth, chronic sinus infection.

When phenylalanine builds up it affects brain functions and the central nervous system. Some symptoms include: skin problems, neurological impairment, seizures, development delays and mental retardation.

2. How do the conditions affect the functioning of the digestive system?
CF mainly affects the pancreas. In CF, mucus can block tubes, or ducts in your pancreas, these blockages prevent enzymes from reaching your intestines. As a result your intestines cant fully absorb fats and proteins. This can cause ongoing diarrhea or bulky, foul-smelling greasy stools. Intestinal blockages also may occur, especially in new borns.

In people with PKU , a particular enzymes used to break down Phenylalanine doesn’t work so the phenylalanine doesn’t get broken down, so the amino acid builds up in the body and in the brain which can cause growth and development problems.

3. What diet modifications are required for each condition?
People with CF need to eat more than most other people and they usually plan what they eat, it is very important that the meal contains high calories and far and that the person with CF does not miss a meal. Kids with Cf need more calories and fats to grow and gain weight as they have a harder time developing than normal kids. Kids with CF must have these nutrients in their diets: Iron, Zinc, Calcium and salt.

People with PKU must follow a special low-protein diet, so they are not a lot to eat milk , eggs, cheese, soy, beans, beef and other meats, fish, chocolate , peas, some medications, and sodas and they are only aloud to ingest foods such as fruits , vegetables,

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