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Cystic Fibrosis Research Paper

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Cystic Fibrosis Research Paper
Cystic fibrosis is a progressive, genetic disease that causes persistent lung infections and limits the ability to breathe over time. This condition leads to excessive production and accumulation of thick persistent mucus in the tracheobronchial tree. The mucous instead of normally being thin and slippery becomes so stiff and rigorous that adequate mucociliary clearance becomes almost impossible. Leading to mucus plugging in the bronchi and bronchioles. The cystic fibrosis foundations says:
“In people with CF, a defective gene causes a thick, buildup of mucus in the lungs, pancreas and other organs. In the lungs, the mucus clogs the airways and traps bacteria leading to infections, extensive lung damage and eventually, respiratory failure.
…show more content…
Starting with some of the respiratory signs and symptoms
“The thick and sticky mucus associated with cystic fibrosis clogs the tubes that carry air in and out of your lungs. This can cause signs and symptoms such as: A persistent , cough that produces thick mucus (sputum), Wheezing, Breathlessness, Exercise intolerance, Repeated lung infections, Inflamed nasal passages or a stuffy nose.”(Mayo Clinic Staff Print)
More complications for CF are damaged airways, chronic infections, palyps, hemoptysis, pneumothorax, respiratory failure, and acute exacerbations. Cystic fibrosis does not only disturb the lungs and airways, it also attacks the digestive system. The thick mucus blocks the passageways of the pancreas stopping the enzymes from being able to reach the small intestine. Ergo the mucus plug constrains the digestion of protein and fat leading to a defect in attaining fat soluble vitamins. To add to the digestive system symptoms are poor weight gain and growth, increased risk of diabetes, intestinal blocking, severe constipation, diarrhea, malnutrition, and frequent straining can lead to rectal prolapse. Reproductive complications can occur in people with cystic fibrosis. Most men are infertile due to missing or mucus blocked vas deferens which connects the testes and prostate gland. Women have less of a chance getting pregnant but still can. Although pregnancy can worsen the signs and symptoms of cystic

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